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Title
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A patient with a severe glottic stenosis and saddle nose
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Author
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Abstract
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| We present the case of a 39-year-old man with a severe glottis stenosis. The saddle nose, images of laryngotracheal stenosis and the (FDG) positron-emission tomography/computed tomography lead to a final diagnosis of relapsing polychondritis. In the patient a coexistent myelodysplastic syndrome was diagnosed. Moreover, the elevated total IgG4 exceeding 135 ml/dl requested additional immunochemistry for detection of IgG4-bearing plasma cells in the biopsies. The patient underwent an allogenic stem cell transplantation and died on day 40 after the transplantation because of an acute steroid-resistent graft vs host. |
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Language
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English
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Source (journal)
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Acta clinica Belgica. - Leuven, 1946 - 1997
Acta clinica Belgica / Belgian Society of Internal Medicine [Ghent]; Royal Belgian Society of Laboratory Medicine. - Gent, 1997, currens
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Publication
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Leuven
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2017
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ISSN
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0001-5512
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DOI
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10.1080/17843286.2015.1111657
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Volume/pages
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72
:2
(2017)
, p. 130-132
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ISI
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000398113200008
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Pubmed ID
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27075792
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Full text (Publisher's DOI)
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Full text (open access)
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Full text (publisher's version - intranet only)
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