Publication
Title
Successful surgical repair of progressive exophthalmos caused by a meningocele in a patient with neurofibromatosis Type 1 - Case report
Author
Abstract
A case of surgical repair of progressive exophthalmos of the right eye in a 43-year-old woman with neurofibromatosis Type 1 (NFI) is presented. Preoperatively, the patient's ocular movements and visual fields were intact. Visual acuity was 20/30 on the right side and 20/20 on the left. Computerized tomography scanning demonstrated complete absence of the superolateral orbital wall on the right side with a large meningocele protruding into the right orbit. Intraoperatively, a new superolateral wall was constructed using the inner table of the left frontal bone as a bone transplant. A free galeoperiosteum flap was used for water-tight dural reconstruction. A few weeks postoperatively the patient's exophthalmos showed remarkable resolution. Her ocular movements, visual acuity, and visual fields remained unchanged. In conclusion, reconstruction of the superolateral wall and repair of a meningocele in a patient with NF1 is worthwhile and can be followed by excellent cosmetic results. More important, the patient's visual functions remain preserved.
Language
English
Source (journal)
Journal of neurosurgery / American Association of Neurological Surgeons [Rolling Meadows, Ill.] - Rolling Meadows, Ill., 1944, currens
Publication
Rolling Meadows, Ill. : American Association of Neurological Surgeons , 1998
ISSN
0022-3085 [print]
1933-0693 [online]
DOI
10.3171/JNS.1998.89.6.1032
Volume/pages
89 :6 (1998) , p. 1032-1035
ISI
000078708200020
Full text (Publisher's DOI)
UAntwerpen
Publication type
Subject
External links
Web of Science
Record
Identifier
Creation 15.10.2019
Last edited 28.08.2024
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